Bone Pathology Database

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2nd image
Detail showing pathological fracture
Third image
Oblique hand XR
The stippled calcifications in the lesions suggest a cartilaginous lesion. There is chronic expansion of the proximal philanges of the index and little fingers. Other hand bones such as the 4th and 5th metacarpal shafts are also involved.
The lesions are most likely enchondromata, and the fact that they are multiple suggests Ollier's Disease.

Ollier's Disease:

characterized by multiple enchondroma lesions primarily located in the metaphyseal regions of tubular bones;
- usually noticed in childhood;
- pts Ollier's disease have increased risk of a secondary chondrosarcoma developing later in life;
- risk is about 25% by age 40 yrs;

- Clinical Findings:
- most patients have bilateral involvement, with often predominance on one side;
- enchondromas most frequently involve the short tubular bones of
hands and feet as well as long bones of upper and lower extremities;
- development of palpable masses, angular deformity & growth disturbances
resulting in angular deformities & leg length discrepancies;
- limb length inequality may be of sufficient severity to require surgery;

Cutettage and bone graft.

Record 79